E71.0✓ Billable

Maple-syrup-urine disease

Also Indexed As(ICD-10-CM Alphabetic Index)

These clinical terms, synonyms, and manifestations all map to E71.0 in the official ICD-10-CM Alphabetic Index.

Disease, diseased, maple-syrup-urineDisorder (of), metabolism NOS, amino-acid, branched chain, maple syrup urine diseaseMaple-syrup-urine diseaseMenkes' disease or syndrome, meaning maple-syrup-urine diseaseSyndrome, maple-syrup-urine

Code Hierarchy

┌4Endocrine, nutritional and metabolic diseases (E00-E89)├E70-E88Metabolic disorders (E70-E88)├E71Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
└E71.0Maple-syrup-urine disease

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