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Disorder
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metabolism NOS
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amino-acid
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branched chain
ICD-10-CM Alphabetic Index
Disorder, metabolism NOS, amino-acid, branched chain
E71.2
Sub-terms
(10)
—
3-methylglutaconic aciduria
E71.111
—
hyperleucine-isoleucinemia
E71.19
—
hypervalinemia
E71.19
—
isovaleric acidemia
E71.110
—
maple syrup urine disease
E71.0
—
methylmalonic acidemia
E71.120
—
organic aciduria NEC
E71.118
—
other specified
E71.19
—
propionate NEC
E71.128
—
propionic acidemia
E71.121
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