Q82.2✓ Billable

Congenital cutaneous mastocytosis

Inclusion Terms

  • Congenital diffuse cutaneous mastocytosis
  • Congenital maculopapular cutaneous mastocytosis
  • Congenital urticaria pigmentosa

Also Indexed As(ICD-10-CM Alphabetic Index)

These clinical terms, synonyms, and manifestations all map to Q82.2 in the official ICD-10-CM Alphabetic Index.

Mastocytosis, cutaneous (diffuse) (maculopapular), congenitalMastocytosis, cutaneous (diffuse) (maculopapular), of neonatal onsetMastocytosis, cutaneous (diffuse) (maculopapular), of newborn onsetUrticaria, pigmentosa, congenitalUrticaria, pigmentosa, of neonatal onsetUrticaria, pigmentosa, of newborn onset

Excludes 1(Not coded here)

  • cutaneous mastocytosis NOS (D47.01)
  • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
  • malignant mastocytosis (C96.2-)
  • systemic mastocytosis (D47.02)
  • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)

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