E78.3✓ Billable
Hyperchylomicronemia
Inclusion Terms
- •Chylomicron retention disease
- •Fredrickson's hyperlipoproteinemia, type I or V
- •Hyperlipidemia, group D
- •Mixed hyperglyceridemia
Also Indexed As(ICD-10-CM Alphabetic Index)
These clinical terms, synonyms, and manifestations all map to E78.3 in the official ICD-10-CM Alphabetic Index.
Bürger-Grütz disease or syndromeChylomicronemia (fasting) (with hyperprebetalipoproteinemia)Disease, diseased, Bürger-Grütz (essential familial hyperlipemia)Disease, diseased, chylomicron retentionFrederickson's hyperlipoproteinemia, type, I and VHepatosplenomegaly, hyperlipemic (Bürger-Grütz type)Hyperchylomicronemia (familial) (primary)Hyperchylomicronemia (familial) (primary), with hyperbetalipoproteinemiaHyperglyceridemia (endogenous) (essential) (familial) (hereditary) (pure), mixedHyperlipemia, hyperlipidemia, group, DHyperlipoproteinemia, Fredrickson's type, IHyperlipoproteinemia, Fredrickson's type, VLipemia, retina, retinalisLipidosis, hepatosplenomegalicPrebetalipoproteinemia (acquired) (essential) (familial) (hereditary) (primary) (secondary), with chylomicronemiaSyndrome, Bürger-GrützXanthoma (s), xanthomatosis (primary) (familial) (hereditary), with, hyperlipoproteinemia, Type IXanthoma (s), xanthomatosis (primary) (familial) (hereditary), with, hyperlipoproteinemia, Type V
Code Hierarchy
Not sure between two codes?
⇄ Compare E78.3 with another code →