E78.3✓ Billable

Hyperchylomicronemia

Inclusion Terms

  • Chylomicron retention disease
  • Fredrickson's hyperlipoproteinemia, type I or V
  • Hyperlipidemia, group D
  • Mixed hyperglyceridemia

Also Indexed As(ICD-10-CM Alphabetic Index)

These clinical terms, synonyms, and manifestations all map to E78.3 in the official ICD-10-CM Alphabetic Index.

Bürger-Grütz disease or syndromeChylomicronemia (fasting) (with hyperprebetalipoproteinemia)Disease, diseased, Bürger-Grütz (essential familial hyperlipemia)Disease, diseased, chylomicron retentionFrederickson's hyperlipoproteinemia, type, I and VHepatosplenomegaly, hyperlipemic (Bürger-Grütz type)Hyperchylomicronemia (familial) (primary)Hyperchylomicronemia (familial) (primary), with hyperbetalipoproteinemiaHyperglyceridemia (endogenous) (essential) (familial) (hereditary) (pure), mixedHyperlipemia, hyperlipidemia, group, DHyperlipoproteinemia, Fredrickson's type, IHyperlipoproteinemia, Fredrickson's type, VLipemia, retina, retinalisLipidosis, hepatosplenomegalicPrebetalipoproteinemia (acquired) (essential) (familial) (hereditary) (primary) (secondary), with chylomicronemiaSyndrome, Bürger-GrützXanthoma (s), xanthomatosis (primary) (familial) (hereditary), with, hyperlipoproteinemia, Type IXanthoma (s), xanthomatosis (primary) (familial) (hereditary), with, hyperlipoproteinemia, Type V

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