E72.4✓ Billable
Disorders of ornithine metabolism
Inclusion Terms
- •Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome
- •Ornithinemia (types I, II)
- •Ornithine transcarbamylase deficiency
Also Indexed As(ICD-10-CM Alphabetic Index)
These clinical terms, synonyms, and manifestations all map to E72.4 in the official ICD-10-CM Alphabetic Index.
Deficiency, deficient, ornithine transcarbamylaseDisorder (of), metabolism NOS, amino-acid, ornithineDisorder (of), metabolism NOS, ornithineDisorder (of), ornithine metabolismDisorder (of), urea cycle metabolism, ornithine transcarbamylase deficiencyDisturbance (s), metabolism, ornithineHyperaminoaciduria, ornithineHyperornithinemiaOrnithine metabolism disorderOrnithinemia (Type I) (Type II)Syndrome, hyperammonemia-hyperornithinemia-homocitrullinemia
✗ Excludes 1(Not coded here)
- •hereditary choroidal dystrophy (H31.2-)
Code Hierarchy
┌4Endocrine, nutritional and metabolic diseases (E00-E89)├E70-E88Metabolic disorders (E70-E88)├E72Other disorders of amino-acid metabolism
└E72.4Disorders of ornithine metabolism
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