Block · Chapter 3
D80-D89Certain disorders involving the immune mechanism (D80-D89)
100 codes · 7 categories
D80Immunodeficiency with predominantly antibody defects11 codes →
D80Immunodeficiency with predominantly antibody defectsHeaderD80.0Hereditary hypogammaglobulinemiaBillableD80.1Nonfamilial hypogammaglobulinemiaBillableD80.2Selective deficiency of immunoglobulin A [IgA]BillableD80.3Selective deficiency of immunoglobulin G [IgG] subclassesBillableD80.4Selective deficiency of immunoglobulin M [IgM]BillableD80.5Immunodeficiency with increased immunoglobulin M [IgM]BillableD80.6Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemiaBillableD80.7Transient hypogammaglobulinemia of infancyBillableD80.8Other immunodeficiencies with predominantly antibody defectsBillableD80.9Immunodeficiency with predominantly antibody defects, unspecifiedBillable
D81Combined immunodeficiencies21 codes →
D81Combined immunodeficienciesHeaderD81.0Severe combined immunodeficiency [SCID] with reticular dysgenesisBillableD81.1Severe combined immunodeficiency [SCID] with low T- and B-cell numbersBillableD81.2Severe combined immunodeficiency [SCID] with low or normal B-cell numbersBillableD81.3Adenosine deaminase [ADA] deficiencyHeaderD81.30Adenosine deaminase deficiency, unspecifiedBillableD81.31Severe combined immunodeficiency due to adenosine deaminase deficiencyBillableD81.32Adenosine deaminase 2 deficiencyBillableD81.39Other adenosine deaminase deficiencyBillableD81.4Nezelof's syndromeBillableD81.5Purine nucleoside phosphorylase [PNP] deficiencyBillableD81.6Major histocompatibility complex class I deficiencyBillableD81.7Major histocompatibility complex class II deficiencyBillableD81.8Other combined immunodeficienciesHeaderD81.81Biotin-dependent carboxylase deficiencyHeaderD81.810Biotinidase deficiencyBillableD81.818Other biotin-dependent carboxylase deficiencyBillableD81.819Biotin-dependent carboxylase deficiency, unspecifiedBillableD81.82Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]BillableD81.89Other combined immunodeficienciesBillableD81.9Combined immunodeficiency, unspecifiedBillable
D82Immunodeficiency associated with other major defects8 codes →
D82Immunodeficiency associated with other major defectsHeaderD82.0Wiskott-Aldrich syndromeBillableD82.1Di George's syndromeBillableD82.2Immunodeficiency with short-limbed statureBillableD82.3Immunodeficiency following hereditary defective response to Epstein-Barr virusBillableD82.4Hyperimmunoglobulin E [IgE] syndromeBillableD82.8Immunodeficiency associated with other specified major defectsBillableD82.9Immunodeficiency associated with major defect, unspecifiedBillable
D83Common variable immunodeficiency6 codes →
D83Common variable immunodeficiencyHeaderD83.0Common variable immunodeficiency with predominant abnormalities of B-cell numbers and functionBillableD83.1Common variable immunodeficiency with predominant immunoregulatory T-cell disordersBillableD83.2Common variable immunodeficiency with autoantibodies to B- or T-cellsBillableD83.8Other common variable immunodeficienciesBillableD83.9Common variable immunodeficiency, unspecifiedBillable
D84Other immunodeficiencies10 codes →
D84Other immunodeficienciesHeaderD84.0Lymphocyte function antigen-1 [LFA-1] defectBillableD84.1Defects in the complement systemBillableD84.8Other specified immunodeficienciesHeaderD84.81Immunodeficiency due to conditions classified elsewhereBillableD84.82Immunodeficiency due to drugs and external causesHeaderD84.821Immunodeficiency due to drugsBillableD84.822Immunodeficiency due to external causesBillableD84.89Other immunodeficienciesBillableD84.9Immunodeficiency, unspecifiedBillable
D86Sarcoidosis15 codes →
D86SarcoidosisHeaderD86.0Sarcoidosis of lungBillableD86.1Sarcoidosis of lymph nodesBillableD86.2Sarcoidosis of lung with sarcoidosis of lymph nodesBillableD86.3Sarcoidosis of skinBillableD86.8Sarcoidosis of other sitesHeaderD86.81Sarcoid meningitisBillableD86.82Multiple cranial nerve palsies in sarcoidosisBillableD86.83Sarcoid iridocyclitisBillableD86.84Sarcoid pyelonephritisBillableD86.85Sarcoid myocarditisBillableD86.86Sarcoid arthropathyBillableD86.87Sarcoid myositisBillableD86.89Sarcoidosis of other sitesBillableD86.9Sarcoidosis, unspecifiedBillable
D89Other disorders involving the immune mechanism, not elsewhere classified29 codes →
D89Other disorders involving the immune mechanism, not elsewhere classifiedHeaderD89.0Polyclonal hypergammaglobulinemiaBillableD89.1CryoglobulinemiaBillableD89.2Hypergammaglobulinemia, unspecifiedBillableD89.3Immune reconstitution syndromeBillableD89.4Mast cell activation syndrome and related disordersHeaderD89.40Mast cell activation, unspecifiedBillableD89.41Monoclonal mast cell activation syndromeBillableD89.42Idiopathic mast cell activation syndromeBillableD89.43Secondary mast cell activationBillableD89.44Hereditary alpha tryptasemiaBillableD89.49Other mast cell activation disorderBillableD89.8Other specified disorders involving the immune mechanism, not elsewhere classifiedHeaderD89.81Graft-versus-host diseaseHeaderD89.810Acute graft-versus-host diseaseBillableD89.811Chronic graft-versus-host diseaseBillableD89.812Acute on chronic graft-versus-host diseaseBillableD89.813Graft-versus-host disease, unspecifiedBillableD89.82Autoimmune lymphoproliferative syndrome [ALPS]BillableD89.83Cytokine release syndromeHeaderD89.831Cytokine release syndrome, grade 1BillableD89.832Cytokine release syndrome, grade 2BillableD89.833Cytokine release syndrome, grade 3BillableD89.834Cytokine release syndrome, grade 4BillableD89.835Cytokine release syndrome, grade 5BillableD89.839Cytokine release syndrome, grade unspecifiedBillableD89.84IgG4-related diseaseBillableD89.89Other specified disorders involving the immune mechanism, not elsewhere classifiedBillableD89.9Disorder involving the immune mechanism, unspecifiedBillable